TITLE:
Clear cell sarcoma of the jejunum—Surgical management in two patients with review of the literature
AUTHORS:
Anupama Mehta, Kirstyn Brownson, Razan Massarani, Thomas Esposito, Gerard Abood, Margo Shoup
KEYWORDS:
Clear Cell Sarcoma; Lymph Node Metastasis; Gastrointestinal Tract
JOURNAL NAME:
Case Reports in Clinical Medicine,
Vol.2 No.4,
July
19,
2013
ABSTRACT: Clear cell sarcoma is
usually described as a malignant melanoma of the soft tissues. The overall
prognosis is poor because of delay in diagnosis and vague clinical symptoms. It
is rarely involved in the gastrointestinal tract, and its diagnosis is
often missed secondary to infrequent occurrence and histological resemblance
to melanoma. We present two cases of primary CCS of
the jejunum whose clinical presentations were
complicated by lymph node involvement. Prompt diagnosis and potential
aggressive surgical intervention may improve overall survival.