TITLE:
Epitheloid Leiomyosarcoma of the Jejunum Presenting with Intussusception in a Young Adult Male: A Case Report
AUTHORS:
John O. Obafunwa, Christopher Pritchett, Siva Maikandanathan, Dahiru Adamu Garkuwa
KEYWORDS:
Epitheloid Leiomyosarcoma; Intussusception; Surgical Resection
JOURNAL NAME:
Surgical Science,
Vol.4 No.5,
May
7,
2013
ABSTRACT: A 27-year-old male presented with intestinal obstruction due
to a jejuno-jejunal intussusception, 23 years after a childhood nasopharyngeal
carcinoma. He was successfully treated for the latter by radiotherapy but
subsequently required a mandibuloplasty for presumably facial hypoplasia sequel
to the radiotherapy. The present intussusception was resected with wide margins revealing a
partly haemorrhagic, polypoid and sessile jejunal tumour measuring 7.7 × 3.5 × 2.6 cm. Microscopy with extensive
immunohistochemical studies revealed a relatively rare and highly malignant epitheloid
leiomyosarcoma arising from the muscularis propria with extension to the mucosa
and serosa. No metastases were found and post-operative follow-up has so far
been uneventful. The present case of a
malignant tumour presenting as an intussusception in a young adult, was
unrelated to a childhood malignant tumour in the same patient. The former was
successfully treated by a wide excision in support of the advocated surgical
approach to adult intussusception.