TITLE:
Malignant Triton Tumor in the Abdominal Wall: A Case Report
AUTHORS:
Yoshiyuki Kitamura, Koichiro Abe, Shingo Baba, Takuro Isoda, Yasuhiro Maruoka, Yoshio Matsuo, Yuichiro Kubo, Akio Sakamoto, Hiroshi Nishimura, Masayuki Sasaki, Hiroshi Honda
KEYWORDS:
Malignant Triton Tumor (MTT); Malignant Peripheral Nerve Sheath Tumor (MPNST); 2-[F-18]-Fluoro-2-Deoxy-D-Glucose Positron Emission Tomography/Computed Tomography (FDG-PET/CT)
JOURNAL NAME:
Advances in Molecular Imaging,
Vol.3 No.2,
April
12,
2013
ABSTRACT: Malignant triton tumor (MTT) is a rare variant of malignant peripheral nerve sheath tumor (MPNST) with rhabdomyosarcomatous differentiation. We report the case of a 54-year-old male without a history of neurofibromatosis type 1 (NF1) who had a growing abdominal wall tumor diagnosed as MTT. Computed tomography (CT), magnetic resonance imaging (MRI) and 2-[F-18]-fluoro-2-deoxy-D-glucose positron emission tomography/CT (FDG-PET/CT) were performed. The MRI and FDG-PET/CT indicated that the lateral component of the tumor was composed of many proliferative cells, corresponding to the histopathological finding of a cellular proliferation of spindle-shaped cells. In light of this case and previous reports, it is apparent that FDG-PET/CT is a helpful tool for distinguishing MTT from benign peripheral nerve sheath tumor.