TITLE:
Desmoplastic small round cell tumor of the abdomen: A case report and literature review of therapeutic options
AUTHORS:
Hafida Benhammane, Leila Chbani, Abdelmalek Ousadden, Ouadii Mouquit, Siham Tizniti, Afaf Riffi Amarti, Nouafal Mellas, Omar El Mesbahi
KEYWORDS:
Desmoplastic Small Round Cell Tumor; Abdomen; Histology; Chemotherapy; Surgery; Outcome
JOURNAL NAME:
Health,
Vol.4 No.4,
April
26,
2012
ABSTRACT: Desmoplastic small round cell tumor (DSRCT) is a rare and highly aggressive variety of sarcoma arising typically from abdominal or pelvic peritoneum. Diagnosis and treatment approaches of this entity are complex and require a skilled, experienced, multidisciplinary team. Authors report their experience with a case of an intraabdominal DSRCT arising in a 37-year-old young man in order to discuss the clinico-pathological and radiological behavior of this tumor and underline diagnostic and therapeutic difficulties.