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Emre, S., Özcan, R., Bakır, A.C., Kuruğoğlu, S., Çomunoğlu, N., Şen, H.S., Celkan, T. and Tekantaa, G.T. (2020) Adrenal Masses in Children: Imaging, Surgical Treatment and Outcome. Asian Journal of Surgery, 43, 207-212.
has been cited by the following article:
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TITLE:
Corticosurrenaloma: About a Pediatric Case
AUTHORS:
Thierry Mukenge Wa Mukengeshay, Fatoumata Binta Balde, Zineb Benmassaoud, Priscilla Kinsala, Othmane Allaoui, Abdelhalim Mahmoudi, Khalid Khattala, Sara Benmilloud, Youssef Bouabdallah
KEYWORDS:
Adrenal Tumor, Adrenal Cortex, Hyperandrogenism, Child
JOURNAL NAME:
Open Journal of Pediatrics,
Vol.12 No.2,
May
24,
2022
ABSTRACT: Introduction: This study aims to describe the outcome of
adrenocortical cancer in children through observation. Observation: A
10-year-old girl with no previous pathological history. She presented headaches
and severe hypertension with clinical and biological signs of hyperandrogenism
for 6 months. An abdominal CT scan showed an encapsulated left adrenal mass
without local or regional invasion or secondary location. A pheochromocytoma or
adrenal neuroblastoma was first suspected. The blood pressure was stable at
130/65 mmHg under antihypertensive drugs. She underwent a complete tumor resection
without any intraoperative incident. The pathologic study confirmed the
adrenocortical carcinoma scored Weiss 7. The severe high blood pressure
reappeared 2-year later despite antihypertensive drugs. The thoracic abdominal
and pelvic CT scan showed a locally advanced tumor recurrence in
the left adrenal gland with parenchymal nodes in the lungs and liver. The
outcome was fatal despite medical and surgical management. Conclusion: Adrenocortical cancer is a rare tumor. It is important to hormonal testing in the presence of Cushing’s syndrome in children. It can give a strong
indication of the diagnostic possibilities. Histology confirms the diagnosis.
The evolution is covered by complications, in particular recurrence with
life-threatening metastases.