TITLE:
Paratesticular Rhabdomyosarcoma in a 30 Months Old Child at the Lagoon Mother and Child Teaching Hospital (CHUMEL) in Cotonou
AUTHORS:
Bognon Gilles, Akodjenou Joseph, Guédénon Medard, Soho Edson, Kunaba Safari Dominique, Gbenou Antoine Séraphin, Alao Jules Maroufou
KEYWORDS:
Tumor, Paratesticular Rhabdomyosarcoma, Treatment, Boy
JOURNAL NAME:
Open Journal of Pediatrics,
Vol.12 No.1,
March
28,
2022
ABSTRACT: Introduction: Rhabdomyosarcoma is the most common soft tissue tumor in children. Modern
multidisciplinary approaches make it possible to better characterize the
different entities and to adapt the treatment accordingly. Paratesticular
localization is rare and aggressive. We report here a case of paratesticular
localization in a 30 months old boy. Observation: The parents would have
noticed a small, painless and rapidly evolving testicular mass in the 6 months
old child. Not having health insurance, they went to the hospital only 5 months
later. This was followed by a total ablation of the mass (without orchidectomy)
and a pleiomorphic rhabdomyosarcoma had been concluded. No chemotherapy was
performed and the mass recurred 2 months later.
This time, its ablation was followed by a series of non-adapted chemotherapy
sessions with irregular follow-ups leading 8 months later to the child’s
admission at our department. He presented with a degraded general condition,
associating an infectious and anemic syndrome, an important increase of the
scrotal mass and the occurrence of a tumoral mass in the left iliac fossa. The
tumoral nature of these masses was confirmed on abdominal ultrasound and scan.
The tumor was classified stage II (TNM: initial Tumors, Nodes, Metastasis). The
multidisciplinary medical staff indicated a total ablation of the two masses,
followed by a new session of adapted chemotherapy, in the absence of
radiotherapy means. The child died in the immediate surgery follow-ups due to
cardiac arrest. Conclusion: In our context of insufficient technical
facilities, only early detection and adapted imperative chemotherapy, would
have enabled a durable remission in front of the paratesticular rhabdomyosarcoma.