Article citationsMore>>

Benson, M.D., Buxbaum, J.N., Eisenberg, D.S., Merlini, G., Saraiva, M.J.M., et al. (2018) Amyloid Nomenclature 2018: Recommendations by the International Society of Amyloidosis (ISA) Nomenclature Committee. Amyloid, 25, 215-219.
https://doi.org/10.1080/13506129.2018.1549825

has been cited by the following article:

• TITLE: AA Amyloidosis Secondary to Primary Sjögren Syndrome: Can It Be Developed without Chronic Inflammation?

  AUTHORS: Soukaina Zaher, Kawtar Nassar, Ibtissam Razzouki, Meriem Regragui, Mehdi Karkouri, Saadia Janani

  KEYWORDS: AA Amyloidosis, Amyloid, Primary Sjögren Syndrome

  JOURNAL NAME: Open Journal of Rheumatology and Autoimmune Diseases, Vol.11 No.2, April 22, 2021

  ABSTRACT: Background: The association of primary Sjögren syndrome (PSS) and AA amyloidosis is a rare occurrence. Objective: To describe the phenotype of patients with this association through our two cases and a literature review. Materials and methods: A report of two cases of AA amyloidosis complicating primary Sjögren syndrome with a literature review. Results: Eight patients of Primary Sjögren’s Syndrome complicated by AA amyloidosis were studies. Six cases were reported in the literature by consulting several databases. 50% of patients had a positive immunological assessment, three cases with kidney damage, and three cases lung damage. Conclusion: The immunological activity in the Primary Sjogren’s Syndrome requires the search not only a lymphoma but also AA amyloidosis apart from any clinical or biological chronic inflammation.