TITLE:
Oeis Syndrome (Cloacal Exstrophy): About Two Cases Treated at the Mother and Child Teaching Hospital in Cotonou (Benin)
AUTHORS:
Antoine Séraphin Gbenou, Beaudelaire Romulus Assan, Joseph Akodjenou, Nicole Tchiakpe Enianloko, Monsoïa Gildas Yasségoungbé, Michel Armand Fiogbe
KEYWORDS:
OEIS Syndrome, Cloacal Exstrophy, Newborn, Prenatal Diagnosis
JOURNAL NAME:
Open Journal of Pediatrics,
Vol.10 No.3,
September
25,
2020
ABSTRACT: Introduction: OEIS syndrome, the most severe form of exstrophy-epispadias complex, is characterized
by the existence of an omphalocele, a bladder exstrophy, an anal imperforation and
a spina bifida. Case Presentation: Two clinical cases admitted at the first
day of life in neonatology department are reported; one was born by caesarean section,
weighing 2500 g and the other one vaginally with a weight at 1890 g. The first child’s
mother was a primigravid, primiparous and the second mother was multiparous. Prenatal
ultrasound was performed in one case. The clinical examination found two exstrophied
hemi-bladders with two productive ureteral meatus, separated by a double intestinal
orifice, a manifestation of anal imperforation, omphalocele, spina bifida and lumbar
vertebral malformations; which corresponds to a typical form of OEIS syndrome. One
of the babies had an associated clubfoot. The karyotype could not be performed.
Both were dead; the first in the early postoperative period, the second one at 16
days of life without surgery. Conclusion: OEIS syndrome is a rare condition
and represents a therapeutic challenge in developing countries. Promoting prenatal
diagnosis is essential.