TITLE:
Corrected Transposition of the Great Arteries with Ebstein’s Anomaly, Dysplasia of the Mitral Leaflets and Persistence of Left Superior Vena Cava in an Adult
AUTHORS:
Aureo Campos-Tello, Giancarlo A. Valle, Luis M. Milla, Angel D. Cueva, Sara Ramirez-Flores, Oscar García-Rosadio, Pablo A. Mendoza, Nilda Espinola-Zavaleta
KEYWORDS:
Corrected Transposition, Echocardiography, Ebstein’s Anomaly, Computed Tomography
JOURNAL NAME:
World Journal of Cardiovascular Diseases,
Vol.10 No.2,
February
13,
2020
ABSTRACT: Introduction: Congenitally corrected transposition of the great arteries (cc-TGA) is a congenital heart disease rarely described among adult population, especially if it is associated with other abnormalities such as Ebstein’s anomaly and abnormal origin of coronary arteries. Case presentation: Twenty-two-year-old woman admitted to intensive care unit with acute decompensated heart failure. The transthoracic echocardiography demonstrated atrioventricular and ventriculoarterial discordance. The left-sided atrioventricular valve, in this case, the tricuspid valve, showed apical displacement of the septal valve suggesting Ebstein’s anomaly. The computed tomography corroborated these findings and additionally showed a left superior vena cava and an abnormal origin of the coronary arteries. The patient is in NYHA functional class II, receiving treatment with diuretic, digitalis, beta-blockers and angiotensin-converting enzyme (ACE) inhibitor. Conclusion: This is a very interesting case of an adult in the third decade of life with cc-TGA associated with abnormalities not described in the literature that had reached adulthood. Noninvasive images play an important role in its diagnosis.