TITLE:
Pleuropulmonary Blastoma in Pediatric Age Group: A Very Rare Case Report and Review of Literature
AUTHORS:
Kalpesh Onkar Patil
KEYWORDS:
Pleuropulmonary Blastoma, Rare Pediatric Lung Cancers, Rare Causes of Solid Lung Lesions
JOURNAL NAME:
Open Journal of Pediatrics,
Vol.10 No.1,
January
31,
2020
ABSTRACT: Pleuropulmonary blastoma
(PPB) is a very rare and very aggressive malignant tumor that affects children
and adults. Though its presentation in children has been reported in literature,
incidence is very low as compared to adults. This neoplasm is characterized on histology by primitive
blastema and a malignant mesenchymal stroma that often demonstrates multidirectional
differentiation. Even though availability of multimodal therapy, the prognosis of patients with PPB remains poor.