TITLE:
Congenital Pulmonary Adenomatoid Malformation: Unusual Revelation
AUTHORS:
M. Echchikhi, H. Essaber, N. Allali, L. Chat
KEYWORDS:
Congenital, Pulmonary, Malformation
JOURNAL NAME:
Open Journal of Clinical Diagnostics,
Vol.9 No.4,
November
26,
2019
ABSTRACT: Congenital pulmonary
adenomatoid malformation (CPAM) is a congenital lung malformation that is
distinguished by abnormal airway patterning during branching morphogenesis. It
may lead to significant morbidity and mortality in infants due to complications
such as pulmonary infections, lung hypoplasia, respiratory distress, and fetal
hydrops. The diagnosis is usually prenatal thanks to morphological ultrasound;
in postnatal, the anomaly may remain asymptomatic or show respiratory signs or
complications. The postnatal diagnosis is based on computed tomography. In this
article, we report a case of congenital pulmonary
adenomatoid malformation in a 7-month-old patient who presented respiratory
distress that is due to voluminous infected pleural effusion. The diagnosis of
CPAM was suspected at the initial CT and confirmed at the control CT that was
realized after treatment of the infection. The therapeutic management of CPAM is
depending on the severity of complications and its evolution.