TITLE:
Bernard-Soulier Syndrome in Pregnancy: A Case Report
AUTHORS:
Amanda Vilaverde Perez, Cilomar Martins de Oliveira Filho, Tássia Cividanes Pazinato, Mariana Sbaraini, Edimárlei Gonsales Valério, Sheila Nogueira do Amaral, Fernanda Grossi, Daniela Vanessa Vettori, Janete Vettorazzi
KEYWORDS:
Bernard-Soulier, Hemostasis, Thrombocytopenia, Pregnancy, Obstetrics, Postpartum Hemorrhage
JOURNAL NAME:
Open Journal of Obstetrics and Gynecology,
Vol.9 No.6,
June
14,
2019
ABSTRACT: Background: Bernard-Soulier Syndrome (BSS) is a rare autosomal recessively inherited
bleeding disorder of platelet function. Pregnancy in BSS is associated with a
high risk of serious bleeding for both mother and neonate, and current data
show no consensual approach. Aim: To report the case of a pregnant woman with BSS, in order to provide more
information about management of these cases. Case Presentation:
This case report describes a successful pregnancy outcome in a woman with BSS
who was closely monitored throughout pregnancy and postpartum period, and had a
judiciously planned birth. Conclusion: Management of BSS during
pregnancy is still unclear. However, it is important to strictly control
platelet counts and plan the birth in advance.