TITLE:
Transcatheter Decompression of the Left Atrium in an Adolescent with a Double Inlet Left Ventricle, Severe Parachute Mitral Valve Stenosis and Pulmonary Hypertension
AUTHORS:
Y. H. Cai, Q. Li, Z. Li, G. Yang, D. Schranz
KEYWORDS:
Double Inlet Left Ventricle, Parachute Mitral Valve, Pulmonary Hypertension, Left Atrial Decompression
JOURNAL NAME:
World Journal of Cardiovascular Diseases,
Vol.7 No.12,
December
14,
2017
ABSTRACT: A 17-year-old adolescent with non-operated double inlet left-ventricle and severe stenosed parachute mitral valve is reported. He was admitted with repetitive syncope related to intermittent atrial fibrillation. Life-threatening syncope combined with pre- and post-capillary pulmonary hypertension together with his single ventricle pathophysiology led to the decision for left atrial decompression by percutaneous static atrial septum ballooning after transseptal needle perforation. Aiming to create a restrictive atrial septum defect, unloading of the left atrium without disturbing the balanced hemodynamics was directed for a long-term palliation or as a basis for a further surgical follow-up approach.