TITLE:
Pelvic Multifocal Primitive Bone Epithelioid Angiosarcoma (Iliac Crest and Hip) about One Case and Literature Review
AUTHORS:
Samba Koné, Abidou Coulibaly, Nawe Astride Ngandeu, Kouadio J. N’dah, Stanislas Touré, Adoulaye Bana, Serge Agoh, N’zué Kouakou
KEYWORDS:
Epithelioid Angiosarcoma, Bone, Primitive, Multifocal
JOURNAL NAME:
Open Journal of Pathology,
Vol.7 No.3,
July
24,
2017
ABSTRACT: Epithelioid angiosarcoma is a rare vascular tumour with dark prognosis at short term. The primitive bone localization is exceptional and sometimes presents itself under a unifocal form. We report a clinical case of pelvic multifocal primitive bone epithelioid angiosarcoma (iliac crest and hip) diagnosed on a young male adult (45 years old). The radiological investigations put in evidence geographic osteolytic lesions (type IC) and, diagnostic was given thanks to the histological examination of the surgical biopsy pieces. The evolution was marked by the appearance of pulmonary and lymph node metastases with a death occurring in less than 4 months. Extremely rare tumour, bone epithelioid angiosarcoma is a variant of angiosarcoma characterised by an aggressive nature whose evolution is always fatal. Through this observation we report our experience on the diagnostic approach; and using a literature review we discuss the therapeutic modalities of this tumour with very bad prognosis.