TITLE:
SC Hemoglobinopathy (HbSC) with Osteoarticular Complications: Case Report
AUTHORS:
Filipe Bezerra Macedo, Jucier Gonçalves Júnior, Fabiana Gouveia Guimarães, Raphael Cisne Tomaz, Débora Valentim Monte Alto, Paula Pessoa Pinheiro, Jácia Maria Neves Coelho
KEYWORDS:
SC Hemoglobinopathy, Paediatrics, Case Report
JOURNAL NAME:
Health,
Vol.9 No.7,
July
20,
2017
ABSTRACT: Background: Among hemoglobinopathies, the most prevalent in our population
are hemoglobins S and C, which are capable of producing disease when
homozygous. In cases of double heterozygotes with sickle hemoglobin C (SC),
the disease is less expressive in its clinical condition and rarer. Case report:
Patient has a previous hospitalization with pain in the joints in knee and hip
and several febrile peaks. Upon physical examination, the patient had difficulty
in walking, without edema, pedal and tibial posterior pulses present,
with no signs of compartment syndrome. Complementary exams revealed
anemia, leukocytosis and lymphopenia. The hemoglobin electrophoresis
showed the SC Hemoglobinopathy. The treatment with antibiotic therapy according
to the protocol (Oxacillin and Ceftriaxone) was restarted and submitted
to joint drainage in affected limb. Conclusion: Osteomyelitis and septic
arthritis in patients in the pediatric age group should be considered as serious
infections that deserve hospitalization and more expressive treatment.