TITLE:
Angioid Streaks in Psuedoxanthoma Elasticum
AUTHORS:
Mehrdad Mohammadpour, Nazanin Ebrahimiadib, Seyed Ali Tabatabaei, Mohammad Soleimani, Shima Dehghani, Fatemeh Abdi, Ghasem Saeedi Anari, Amir Hasan Matini, Mahyar Noorbakhsh, Zahra Ghomi
KEYWORDS:
Pseudoxanthoma Elasticum (PXE), Angioid Streaks, Drusen
JOURNAL NAME:
Open Journal of Ophthalmology,
Vol.7 No.1,
February
23,
2017
ABSTRACT: Pseudoxanthoma elasticum (PXE) is a hereditary disorder that affects primarily the elastic tissues of skin, eyes and blood vessels. Its estimated prevalence is thought to be 1:25,000 - 100,000. PXE patients also carry an increased risk for cardiovascular and gastrointestinal diseases. Early diagnosis can play a crucial role in preventing early loss of vision and systemic complications in these patients however despite having characteristic clinical features; it is still to a large extent being under-diagnosed. Here we present two cases of PXE with reduced vision.