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Guay-Woodford, L.M. (2014) Autosomal Recessive Polycystic Kidney Disease: The Prototype of the Hepato-Renal Fibrocystic Diseases. Journal of Pediatric Genetics, 3, 89-101.

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• TITLE: Caroli Disease: A Case Report Observed at the Cocody Teaching Hospital of Abidjan (Cote D’Ivoire)

  AUTHORS: A. Ouattara, S. Koné, E. Allah-Kouadio, D. Soro, A. W. Ndjitoyap, E. Kouadio, K. A. Kanga, C. D. Fanou, M. J. Lohoues-Kouacou, B. M. Camara

  KEYWORDS: Carolisyndrom, Congenital Cystic Dilation, Cholangitis, Liver CT-Scan

  JOURNAL NAME: Open Journal of Gastroenterology, Vol.7 No.1, January 22, 2017

  ABSTRACT: Caroli disease is a rare affection. It’s commonly associated to polycystic kidneys. We report a case of a nine-year-old girl. She was hospitalized at the pediatric unit of the Cocody Teaching Hospital for an intermittent fever. During the clinical examination, we found a likely cirrhotic hepatomegaly associated to an edematous-ascitic syndrome. Biological exams showed an infectious syndrome with a hyperleukocytosis at 13.000 per mm3, a hyperneutrophilia at 9.600 per mm3. Serological viral markers of B, C and D hepatitis were negative. We saw an intra-hepatic cystic picture at the liver CT-scan with a vascular lesion at his center called a “dot sign”. The diagnosis of Caroli disease could be evocated.