TITLE:
Caroli Disease: A Case Report Observed at the Cocody Teaching Hospital of Abidjan (Cote D’Ivoire)
AUTHORS:
A. Ouattara, S. Koné, E. Allah-Kouadio, D. Soro, A. W. Ndjitoyap, E. Kouadio, K. A. Kanga, C. D. Fanou, M. J. Lohoues-Kouacou, B. M. Camara
KEYWORDS:
Carolisyndrom, Congenital Cystic Dilation, Cholangitis, Liver CT-Scan
JOURNAL NAME:
Open Journal of Gastroenterology,
Vol.7 No.1,
January
22,
2017
ABSTRACT: Caroli disease is a rare affection. It’s commonly
associated to polycystic kidneys. We report a case of a nine-year-old girl. She
was hospitalized at the pediatric unit of the Cocody Teaching Hospital for an
intermittent fever. During the clinical examination, we found a likely
cirrhotic hepatomegaly associated to an edematous-ascitic syndrome. Biological
exams showed an infectious syndrome with a hyperleukocytosis at 13.000 per mm3, a
hyperneutrophilia at 9.600 per mm3. Serological viral markers of B,
C and D hepatitis were negative. We saw an intra-hepatic cystic picture at the
liver CT-scan with a vascular lesion at his center called a “dot sign”. The
diagnosis of Caroli disease could be evocated.