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Lenders, J.W., Duh, Q.Y., Eisenhofer, G., Gimenez-Roqueplo, A.P., Grebe, S.K., Murad, M.H., Naruse, M., Pacak, K. and Young, W.F.J. (2014) Pheochromocytoma and Paraganglioma: An Endocrine Society Clinical Practice Guideline. Endocrine Society. The Journal of Clinical Endocrinology and Metabolism, 99, 1915-1942.

has been cited by the following article:

• TITLE: Cardiac Paraganglioma—A Rare Subset of a Rare Tumor

  AUTHORS: Alecsandra-Anca Tudor, Joëlle Tschui, Jürg Schmidli, Ralph A. Schmid, Patrick Dorn

  KEYWORDS: Cardiac Paraganglioma, Paraganglioma

  JOURNAL NAME: World Journal of Cardiovascular Diseases, Vol.7 No.1, January 19, 2017

  ABSTRACT: Background: Cardiac paraganglioma is a rare entity of an uncommon neuroendocrine tumor. Clinically, non-secreting tumors are often diagnosed because of their growth effects, secreting tumors present symptoms related to catecholamine. Correct diagnosis of a paraganglioma can be reached by biochemical investigations and imaging. Surgical resection is the treatment of choice and has to be planned carefully and interdisciplinarily. Aim: On the basis of a patient with a vague clinical presentation and an unclear situation after primary investigations, we highlight the diagnostic challenge of this rare subset of paragangliomas. Case presentation: We present the case of a 42-year-old woman whose unspecific symptoms and further investigations revealed a paracardiac mass with unknown local behavior and dignity. Surgical resection and histopathological examination led to the diagnosis of a cardiac paraganglioma. Conclusion: Cardiac paragangliomas are extremely rare, but may be treated curatively by resection after careful preoperative investigation and interdisciplinary planning.