TITLE:
Anesthetic Consideration of a Patient with McCune-Albright Syndrome: A Case Report
AUTHORS:
Se Hee Kang, Ji Seon Jeong
KEYWORDS:
Difficult Intubation, Fibrous Dysplasia, McCune-Albright Syndrome
JOURNAL NAME:
Open Journal of Anesthesiology,
Vol.6 No.11,
November
30,
2016
ABSTRACT: The McCune-Albright syndrome is rare disease diagnosed
by the clinical triad, fibrous dysplasia, café-au lait skin pigmentations and
endocrine hyperfunction. Those patients with bone issues could have various surgeries
under general anesthesia. Airway abnormality and various endocrine
abnormalities should be considered during general anesthesia for McCune-Albright
syndrome patients. A 15-year-old male with McCune-Albright syndrome was
admitted with complaint of right nasal obstruction originated from fibrous dysplasia.
Endoscopic resection of nasal cavity lesion was scheduled under navigation
system guidance. Difficult airway could be anticipated due to protrusion of
maxilla and right nostril. Awake fiberoptic intubation was performed by spray-as-you-go
technique. When an anesthesiologist expects to take care of the patient
with the McCune-Albright syndrome, the most appropriate anesthetic induction
and tracheal intubation technique should be selected, and multiple backup instruments
such as supraglottic device, video laryngoscope and fiberoptic bronchoscopy
should be prepared.