TITLE:
A Pierre Robin Syndrome with Absent Anterior 2/3 Tongue—A Case Report
AUTHORS:
K. Surender, K. Vasudev, B. Balaram, C. H. Vijay Raj, Lingaiah Jadi
KEYWORDS:
Micrognathia, Glossoptosis, Pierre Robin Sequence
JOURNAL NAME:
International Journal of Otolaryngology and Head & Neck Surgery,
Vol.4 No.6,
November
23,
2015
ABSTRACT: The triad of micrognathia, glossoptosis and airway obstruction originally described in 1923 by Pierre Robin, is known as Robin sequence (or Pierre robin sequence “PRS”). PRS is characterized by micrognathia (small and symmetrical receded mandible), glossoptosis (tongue of variable size falls backwards into the post pharyngeal wall), and cleft palate (U or V shaped). We report a case of 2 hours old newborn presented with micrognathia, retrognathia, and glossoptosis and absent anterior two thirds of tongue.