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has been cited by the following article:

• TITLE: Anesthetic Management of a Boy with Congenital Disorder of Glycosylation (CDG) I-x

  AUTHORS: Amit Lehavi, Hanna Mandel, Yeshayahu (Shai) Katz

  KEYWORDS: Anesthesia, Pediatric, Metabolic Disorders, Congenital Disorders of Glycosylation, CDG

  JOURNAL NAME: International Journal of Clinical Medicine, Vol.2 No.3, July 21, 2011

  ABSTRACT: Congenital disorders of glycosylation (CDGs) are group group of genetic defects in the assembly and processing pathway of protein glycosylation, which cause a wide range of multi system dysfunction. This paper describes the anesthetic management of 6 year old boy with CDG type I-x for upper airway surgery. We used a sevoflurane-nitrous oxide-remifentanil regime with no complications and good results. As for now, the literature lacks reports of anesthetic management of children with CDG I-x, and this report may provide clinicians an option for safe anesthetic management.