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Dyke, C.G., Davidoff, L.M. and Masson, C.B. (1933) Cerebral Hemiatrophy with Homolateral Hypertrophy of the Skull and Sinuses. Surgery, Gynecology & Obstetrics, 57, 588-600.

has been cited by the following article:

• TITLE: Dyke Davidhoff Masson Syndrome Presenting in Adulthood: A Case Report

  AUTHORS: Monika Jawanjal, Nilesh Walke, Archana Bhate, Avinash Jawanjal

  KEYWORDS: Dyke Davidhoff Masson Syndrome, Cerebral Hemiatrophy, Childhood Hemiplegia

  JOURNAL NAME: Open Journal of Clinical Diagnostics, Vol.5 No.2, May 29, 2015

  ABSTRACT: Dyke Davidhoff Masson syndrome (DDMS) was first described by Dyke Davidhoff and Masson in 1933 in a series of 9 patients [1]. It’s a very rare condition presenting in childhood ranging from infancy to late adolescence [2]. It is characterised by cerebral hemiatrophy, unilateral ventriculomegaly, calvarial thickening, skull and facial asymmetry, sometimes even contralateral hemiplegia in childhood and seizures [2]. An adult presentation is seen in late adolescence or teen age. However in literature the latest presentation reported so far is at 19 years of age [3]. We report a case of Dyke Davidhoff Masson syndrome who presented first time at the age of 28 years which is probably the oldest presentation of this rare entity reported in the literature.