TITLE:
Pneumonectomy in a Patient with Swyer-James-MacLeod Syndrome
AUTHORS:
Mariana Vigiola Cruz, Gregory D. Trachiotis
KEYWORDS:
Swyer-James, Hyperlucent Lung, Pneumonectomy
JOURNAL NAME:
Surgical Science,
Vol.6 No.2,
February
11,
2015
ABSTRACT: Swyer-James-MacLeod syndrome is a rare
disease that results in parenchymal damage believed to be caused by recurrent
lung infections in childhood. We report a case of a previously healthy young
woman that presented with insidious progression of exertional dyspnea with
restrictive lung physiology. Axial imaging demonstrated a hyperinflated
emphysematous right lung with lower lobe fibrosis, nodules and air-fluid filled
cysts, with a small right pulmonary artery and contralateral shifting of the
mediastinum. She underwent right pneumonectomy ultimately resulting in improvement of her symptoms, with
surgical pathology indicating extensive emphysema, bronchiec- tasis, fibrosis with osseous
metaplasia, and placental transmogrification of alveolar septa, being
consistent with a diagnosis of SJMS.