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Norioka, M., Kitamura, S., Sumikawa, K., Nagai, H., Amakata, Y., Ota, S., Kosugi, K. and Harano, Y. (1981) EMG Syndrome and Anesthesia (Author’s Translation). Masui, 30, 1243-1248.

has been cited by the following article:

• TITLE: Anesthetic Management of a Child with Simpson-Golabi-Behmel Syndrome—A Case Report

  AUTHORS: Yoshihiro Morita, Kyoko Naito, Natsuko Kimoto, Eiji Kimoto, Tetsuji Omata, Nobuo Morita, Masashi Nakagawa

  KEYWORDS: Simpson-Golabi-Behmel Syndrome, Anesthetic Management, Macroglossia

  JOURNAL NAME: Open Journal of Anesthesiology, Vol.5 No.2, February 4, 2015

  ABSTRACT: Simpson-Golabi-Behmel syndrome (SGBS) is an X-linked recessive condition associated with pre-natal and postnatal overgrowth with visceral and skeletal anomalies. Abnormal airway anatomy may complicate the perioperative management of SGBS. However, there have been few reports regarding the anesthetic management of children with SGBS. We present the preoperative evalua-tion and intraoperative management of a 1.5-year-old child with SGBS undergoing plastic surgery for cleft palate. Sevoflurane-fentanyl anesthesia without a neuromuscular blocker was planned, due to the preoperative evaluation that airway management would be complicated by the macroglossia and short neck characteristic of SGBS. Fortunately, there was no difficulty in endotracheal intubation in the present patient due to careful planning of general anesthesia and meticulous airway management. Appropriate preoperative preparation for a difficult airway by the anesthe-siologist can ameliorate the difficulties inherent to the anesthetic management of patients with SGBS.