TITLE:
Case Report: Propriospinal Myoclonus
AUTHORS:
Catherine Smith, Jason Ramtahal
KEYWORDS:
Myoclonus, PSM, Polymyography
JOURNAL NAME:
Case Reports in Clinical Medicine,
Vol.3 No.6,
June
24,
2014
ABSTRACT: This report
presents a case of propriospinal myoclonus (PSM) in a previously fit and well
female patient who presented with truncal jerking movements when relaxed. Propriospinal
myoclonus is a rare condition, of which 80% of the aetiology is idiopathic. It
is characterised by involuntary jerking movements of the trunk due to spreading
activity via intrinsic propriospinal pathways along the spinal cord.
Polymyography is mandatory in the diagnosis of priopriospinal myoclonus however
in discerning the differential diagnoses it is inferior to magnetic resonance
diffusion tensor imaging. The management of propriospinal myoclonus is
dependent on aetiology. Clonazepam has been shown to be effective in the
treatment of idiopathic PSM for symptomatic relief.