TITLE:
Multicentric Cervical Paraganglioma. Rare Case of Five Locations in One Patient. Case Report and Literature Review
AUTHORS:
José Francisco de Sales Chagas, Maria Beatriz Nogueira Pascoal, José Luis Braga de Aquino, Luis Antonio Brandi Filho, Fernanda Fruet, Douglas Alexandre Rizzanti Pereira, Amilcar de Castro Matos, Thalita Ruba, Fernanda Callegari
KEYWORDS:
Glomus Tumor; Paraganglioma; Glomus Jugulare; Carotid Body Tumor; Postoperative Complications
JOURNAL NAME:
International Journal of Otolaryngology and Head & Neck Surgery,
Vol.3 No.2,
March
27,
2014
ABSTRACT: Objective: To report a case of a multiple
paraganglioma with 5 concurrent locations and also describe a complication not
found in the literature, spontaneous tumor bleeding. Introduction: The
paragangliomas are mostly benign and more frequent in women. Can be multiple,
and these are considered as the most likely source of familial origin (30%-35%). The multicentric lesions can occur at
different life stages not being necessarily simultaneous, a fact that prevents
image exam research to be conclusive for tumor presence or absence. In this way
the examination of the family members of patients, specially young ones,
diagnosed with multicentric tumors may lead to negative results which doesn’t
meant that the disease can be developed at a later time period. Therefore
routine examination is not justifiable when symptoms relative to tumor presence
are not present. Case report: A female patient of 32 years old
complaining of tinnitus and diagnosed with five paragangliomas
(jugulo-timpanic, bilateral carotid body and bilateral brachiocephalic trunk)
through imaging studies. She reported suffering relatives of paragangliomas.
Conclusion: The paper reports a rare case and perhaps unique in the literature,
multiple paraganglioma with five locations and discusses difficult choice of
treatment and complications.