TITLE:
Chronic thromboembolic pulmonary hypertension related to hemangiolymphangioma
AUTHORS:
Tsuneyuki Nakamura, Keita Tamanuki, Giyo Ko, Masato Oguri, Chisato Akita, Chika Kitaoka, Toshimi Nakamura, Yutaka Saikawa
KEYWORDS:
Hemangiolymphangioma; Chronic Thromboembolic Pulmonary Hypertension; Long-Term Follow-Up
JOURNAL NAME:
Case Reports in Clinical Medicine,
Vol.3 No.1,
January
21,
2014
ABSTRACT: Hemangiolymphangioma
(HL) is a congenital anomaly and histologically benign tumor, which was
composed of both the lymphatic and the blood vessels. We report an adult case
of HL complicated by chronic thromboembolic pulmonary hypertension (CTEPH) in
a 20-year-old female. Gastrointestinal bleeding
scintigraphy and operative findings elucidate a close relationship between CTEPH and residual HL. This case indicates
that HL survivors with remaining
left-to-right shunt might lead to CTEPH
during the long-term follow-up.