TITLE:
Challenging management of congenital bilateral radial club hand: A case report
AUTHORS:
Abdulrahman Alhaji Mahmud, Muhammad Kabir Abubakar, Musa Adamu Kabir, Mohammed Inuwa Ismail, Muslimat Ajibola Alada, Bashir Bello
KEYWORDS:
Congenital Radial Club Hand; Centralization; Early Intervention
JOURNAL NAME:
Case Reports in Clinical Medicine,
Vol.3 No.1,
January
21,
2014
ABSTRACT: Congenital radial
club hand (CRCH) is a terminal deficiency characterized by the radial deviation
of the hand, marked shortening of the forearm, and generalized underdevelopment
of the extremity with an incidence rate of 1 per 100,000 live births. Both
sexes are nearly or equally affected. Challenges that the disease poses to the patient
are multifaceted, ranging from medical, social, cosmetic and functional issues
which also are the multidimensional treatment modalities. We report a case of a
2-month-old baby with the severe case of bilateral CRCH. The patient had the centralization of the left ulna with Kwire stabilization. About 160d of correction was achieved. He did well
and was discharged after two weeks at the orthopedic clinic for follow-up. Congenital
radial club hand though uncommon may be amenable to surgery. Centralization is
still the treatment of choice in severe cases and early intervention will offer
a better outcome.