TITLE:
IgG4-Related Disease Presenting as a Soft Tissue Tumor Affecting Skeletal Muscle: A Case Report
AUTHORS:
David Sáez Martínez, Felipe López Oliva, María Jesús Fernández Aceñero, Elena Fontoira Moyer, Juan Luis Arranz Cozar
KEYWORDS:
IgG4-Related Disease; Soft Tissue Mass; Skeletal Muscle
JOURNAL NAME:
International Journal of Clinical Medicine,
Vol.4 No.12A,
December
24,
2013
ABSTRACT:
Background: IgG4-related disease is a systemic lymphoproliferative syndrome that shows
IgG4-producing plasma cell expansion in affected organs with fibrotic or
sclerotic changes. The lacrimal glands, salivary glands and pancreas are
typically affected. We report a case of IgG4-related disease presenting a soft
tissue tumor affecting skeletal muscle. Case Report: A 32-year-old man presented a soft tissue mass
in his left arm. Magnetic resonance imaging revealed a spindle like, peripheral
mass, in the lateral head of the triceps of his left arm. Tru-Cut Biopsy
provided the diagnosis of IgG4-related disease affecting skeletal muscle.
Glucocorticoid treatment was effective. Conclusion: To our knowledge, this is the first reported case of IgG4-related disease
affecting skeletal muscle and presenting a soft tissue mass.