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Leet, A.I., Wientroub, S., Kushner, H., Brillante, B., Kelly, M.H., Robey, P.G., et al. (2006) The correlation of specific orthopaedic features of polyostotic fibrous dysplasia with functional outcome scores in children. The Journal of Bone & Joint Surgery [American], 88, 818-823.
http://dx.doi.org/10.2106/JBJS.E.00259

has been cited by the following article:

• TITLE: Long term treatment of recurring pathological fractures due to Mccune Albright Syndrome: Case report and literature review

  AUTHORS: Yoshvin Sunnassee, Yuhui Shen, Rong Wan, Jianqiang Xu, Weibin Zhang

  KEYWORDS: McCune Albright Syndrome; Surgical Treatment; Polyostotic Fibrous Dysplasia

  JOURNAL NAME: Case Reports in Clinical Medicine, Vol.2 No.9, December 20, 2013

  ABSTRACT: McCune Albright syndrome is a rare genetic disorder which is characterized by café au lait skin pigmentation, precocious puberty and polyostotic fibrous dysplasia. Treating recurring pathological fractures due to Albright syndrome is a very challenging endeavor, and more so when it is accompanied by poor bone quality and deformity. We hereby present the case of a 23-year-old male patient who is treated several times for recurrent pathological fractures of the femur at our center. We analyze the difficulties associated with treating a patient with poor bone quality over several years, discuss our treatment options, review the literature for similar cases and look at what we could have done differently. We weigh in on the difficulties in treating a severely deformed shepherd’s crook, the ways of achieving proper internal fixation and the dangers of using plating instead of an IM nail as suggested in the literature. Our main goal in reporting this case is to bring forth the unusual challenges encountered when treating patients with Albright syndrome and discussing the options of the orthopedic surgeons when treating these types of patients.